Atresia pulmonar con septum integro pdf

Jun 02, 2011 pulmonary atresia and ventricular septal defect and truncus arteriosus lan nguyen, md duration. During pregnancy when the heart is developing, very little blood flows into or out of the right ventricle rv, and therefore the rv doesnt fully develop and remains very small. Pulmonary atresia with intact ventricular septum paivs is a rare congenital malformation. Atresia pulmonar com septo integroatresia pulmonar com septo integro definicao. Atresia pulmonar con septum interventricular integro. Atresia pulmonar con comunicacion interventricular cirugia.

The influence of ventricular morphology and coronary artery dominance and morphology on early mortality in patients with pulmonary atresia and intact ventricular septum. Su reparacion requiere multiples operaciones y cateterismos. Atresia pulmonar con septo integro asociada a estenosis aortica. Atresia pulmonar con septum interventricular intacto scielo cuba.

Pulmonary atresia with intact ventricular septum paivs and critical pulmonary stenosis cps are rare forms of cyanotic congenital heart disease 1,2 where pulmonary blood flow depends on the ductus arteriosus. Pulmonary atresia with intact ventricular septum percutaneous. Pulmonary atresia with intact ventricular septum paivs is a relatively uncommon form of congenital heart disease and is remarkable in its morphologic diversity, characterized by varying degrees of right ventricle rv hypoplasia and associated with tricuspid valve dysplasia and sinusoidal right ventriculocoronary connections. Atresia pulmonar con septo integro francisco portela, sonia marcos cirugia cardiaca infantil y cardiologia infantil complejo hospitalario juan canalejo. Pulmonary atresia and ventricular septal defect and truncus arteriosus lan nguyen, md duration. Gabriel cassalet bustillo, md atresia pulmonar con septo interventricular integro manuel r.

Pdf pulmonary atresia with intact ventricular septum is an apparently simple cyanotic congenital heart disease. Percutaneous management of pulmonary atresia with intact. Atresia pulmonar con septo integro bive ntricular uno y medio glenn univentricular fontan figura 3. Pulmonary atresia with intact interventricular septum paivs is a subtype of pulmonary atresia that presents as cyanotic congenital heart disease. Atresia pulmonar con septum interventricular intacto. Pulmonary atresia with an intact ventricular septum. Gonzalez morejon1 ansia serrano sanchez2 giselle serrano ricardo1.

Atresia pulmonar con comun icacion interventricular gustavo a. Paivs involves complete blockage of the pulmonary valve located on the right side of the heart. Pulmonary atresia with intact ventricular septum and critical pulmonary stenosis in newborns encompasses a wide spectrum of disease, including cases with significant right ventricular hypoplasia and coronary artery to right ventricle fistulae, which may be considered a contraindication for decompression of the right ventricle. Atresia pulmonar con comunicacion interventricular apciv. The pulmonary valve is located on the right side of the heart between the right ventricle and pulmonary artery. Houston methodist debakey cv education 2,7 views 12. There is significant morphologic heterogeneity among patients with paivs, 3 and the selection criteria for univentricular or biventricular repair are under debate. Perforacion y valvuloplastia pulmonar mediante tecnica mecanica modificada. The valve is completely closed thereby obstructing the outflow of blood from the heart to the lungs. Atresia pulmonar con comunicacion interventricular. Pulmonary atresia with intact interventricular septum. In patients with pulmonary atresia with intact ventricular septum paivs, radiofrequencyassisted perforation of the valve is the most widely used initial therapy. Pdf atresia pulmonar con septo integro researchgate. Atresia pulmonar con septo integro connecting repositories.

Atresia pulmonar com comunicacao interventricular cardio. Atresia pulmonar con tabique interventricular integro en una cardiopata congnita ciantica con flujo pulmonar disminuido y cardiomegalia. Atresia pulmonar con septo integro article pdf available in cirugia cardiovascular 212 april 2014 with 43 reads how we measure reads. In this form of pulmonary atresia, the wall, or septum, between the ventricles remains complete and intact. Atresia pulmonar con septo integro biventricular 60% fontan 24% uno y medio 12% paliacion 3% trasplante 1% figura 4. A single uniform approach in the management of this disease is. Pulmonary atresia with intact ventricular septum is an. Congenital heart defects facts about pulmonary atresia cdc. Pathology paivs is the combination of obstruction of the pulmonary outflow tract from pulmona. Atresia pulmonar con septo interventricular intacto y. In a normal functioning heart, the opening to the pulmonary valve has. Atresia pulmonar con tabique interventricular integro.